Doctors rescued a newborn from Khakassia with a very rare heart defect

Krasnoyarsk doctors rescued a newborn with a very rare critical heart defect. The deviation, which was well “maximized” for normal work, was suspected by Khakass doctors and transported a small patient to the Federal Center for Cardiovascular Surgery of the Ministry of Health of the Russian Federation in Krasnoyarsk.

The baby was born at the republican perinatal center in Abakan and immediately after birth came to artificial ventilation of the lungs. For a long time, doctors struggled with congenital infection of the newborn, and when they defeated it, they could not disconnect the child from the ventilator.

The heart defect in the child was very rare and on EchoCG his diagnosis was not just difficult - he was disguised as normal heart function. The only marker was a decrease in oxygenation, that is, blood oxygen saturation and dependence on the drug necessary for critical defects, the cardio center said.

Abakan doctors decided to redirect the baby to Krasnoyarsk for a more accurate diagnosis. There, during an additional examination, a very rare congenital defect (pulmonary-left atrial fistula) was found, in which a significant part of the venous blood enters the artery, which causes a decrease in blood oxygenation.

The operation was successful. The baby has already undergone recovery in the perinatal center of Abakan and even left home.

“Not more than 100 cases of this defect have been described in the literature. At the same time, almost all refer to foreign authors, said Pavel Teplov, head of the children’s department of the Federal Cardiocenter of Krasnoyarsk.

The newborn was on ventilator for more than 20 days (from birth), so rehabilitation was not quick. He was discharged home on the 19th day after the operation.